?Recombinant mouse ACOX1 protein, C-His
重組小鼠過氧化物酶酰基輔酶A氧化酶1蛋白
| 英文名稱 | Recombinant mouse ACOX1 protein, C-His |
| 中文名稱 | 重組小鼠過氧化物酶?；o酶A氧化酶1蛋白 |
| 別????名 | ACOX1; ACOX1_HUMAN; ACOX1_MOUSE; AOX antibody Palmitoyl CoA oxidase; Palmitoyl-CoA oxidase; Peroxisomal acyl coenzyme A oxidase 1; Peroxisomal acyl-coenzyme A oxidase 1; SCOX; Straight chain acyl CoA oxidase; Straight-chain acyl-CoA oxidase. ?? |
| 理論分子量 | 31.8kDa |
| 性????狀 | Lyophilized or Liquid |
| 濃????度 | >0.5mg/ml |
| 物????種 | Mouse |
| 序????列 | 386-661/661 |
| 純????度 | >90% as determined by SDS-PAGE |
| 表達(dá)系統(tǒng) | E.coli |
| 活性 | Not tested |
| 標(biāo)簽 | C-His |
| 緩?沖?液 | 20mM Tris-Hcl (pH=8.0)with 8M Urea |
| 保存條件 | Stored at -70℃ or -20℃. Avoid repeated freeze/thaw cycles. |
| 注意事項 | This product as supplied is intended for research use only, not for use in human, therapeutic or diagnostic applications. |
| 產(chǎn)品介紹 | Defects in ACOX1 are the cause of adrenoleukodystrophy pseudoneonatal (Pseudo-NALD); also known as peroxisomal acyl-CoA oxidase deficiency. Pseudo-NALD is a peroxisomal single-enzyme disorder. Clinical features include mental retardation, leukodystrophy, seizures, mild hepatomegaly, hearing deficit. Pseudo-NALD is characterized by increased plasma levels of very-long chain fatty cids, due to decreased or absent peroxisome acyl-CoA oxidase activity. Peroxisomes are intact and functioning. ? |
| 產(chǎn)品圖片 |
 The purity of the protein is greater than 90% as determined by reducing SDS-PAGE.
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| ? | ? |
本產(chǎn)品僅供科研使用.請勿用于醫(yī)藥,不能用于臨床治療診斷使用！